Study about Late Follow-Up of Persistent Truncus Arteriosus, after One- Stage Repair, Using a Biological Bicuspid Prosthesis to Pulmonary Valve Reconstruction

We report long-term outcomes after one-stage, surgical repair, in a two-month-old girl with Persistent Truncus Arteriosus type I, II. The operation was carried out with the remodeling of the right ventricle, using a swine bicuspid pulmonary prosthesis. Twenty-six years later, the patient is in excellent clinical condition, CF I (NYHA), with normal peripheral oxygen saturation. Recent invasive and not invasive imaging show: Absence of intracardiac shunt and growing of the right ventricle outlet tract and discrete double lesion of the pulmonary valve. The pulmonary flow is directed uniformly for both lungs. In selected cases, the long-term prognosis of patients with truncus arteriosus, undergoing early surgical repair, avoiding the use of valved conduit, makes for an excellent evolution, without new interventions. Endovascular procedures, now well standardized, for the implantation of a pulmonary valve stent, through a catheter, will allow an effective approach, in the presence of late obstructions, in patients who have undergone right ventricular remodeling, without the use of valved conduits. It is concluded that the ventricular remodelling with the reconstruction of the pulmonary valve allowed for the preservation of right ventricular function and the patient's progression to functional class I (NYHA), with no restrictions on her physical activity, over the course of the long follow-up.